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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Differentiation
Autologous
Lamins
Thérapie génique
Myoblasts
Neuromuscular disease
PABPN1 agregates
Ageing
Cell therapy
Myosin
Regulatory T cells
Xenograft
Antisens oligonucleotides
Pharyngeal muscle
Myogenesis
Biomarker
Inflammation
Skeletal muscle
Alphavirus
Sarcopenia
Functional genomics
FSHD
Satellite cells
GENE
Aggregate
Oculopharyngeal muscular dystrophy
Aged
Haploinsufficiency
Accelerometry
Anti-acetylcholine receptor antibodies
Exon-skipping
Myopathies
BINDING SPECIFICITY
Myopathy
Mass spectrometry
Geriatric assessment
Pax7
Fibrosis
Gene replacement
Dystrophin
Epigenetics
Duchenne muscular dystrophy
AChR antibodies
Muscle stem cells
Triplet expansion disease
FAPs
Satellite cell
MUTATIONS
Myoblast
Myotube
DUX4
Bile salt hydrolases
DMD
Antiserum
OPMD
Amyotrophic Lateral Sclerosis
Neuromuscular junction NMJ
Human
Transcriptomics
Metabolism
Autoimmune diseases
Akt
AAV vectors
PABPN1
Annexin A2
Intercellular communication
Alzheimer's disease
ALS
Omics
2-D PAGE
RNA
Muscle strength
Muscle
Dystrophie musculaire oculopharyngée
Adipose tissue
Muscle dystrophy
Dysferlin
Andermann syndrome
Myositis
APOPTOSIS
Dysferlinopathy
Atrophy
Calcium
Muscle fibrosis
AUTOPHAGY
Muscular dystrophy
Cross-bridge kinetics
Actin
Regenerative medicine
Gene therapy
Aav-U7
Nuclear envelope
Effector T cells
Arbovirus
ARN
Anti-fibrotic pharmacotherapies
DNA methylation
AAV
Regeneration
Agrégats de PABPN1